ESPN 50th Annual Meeting

ESPN 2017


 
FIBROMUSCULAR DYSPLASIA – A RARE CAUSE OF RENOVASCULAR HYPERTENSION.
EBRU YILMAZ 1 NIDA DINÇEL 1 ORHAN DENIZ KARA 1 ERKIN SERDAROĞLU 1

1- DR. BEHCET UZ CHILDREN HOSPITAL AND RESEARCH HOSPITAL
 
Introduction:

Fibromuscular dysplasia is a non-atherosclerotic, non-inflammatory disease that most commonly affects the renal and internal carotid arteries. In patients affected by FMD, renal artery aneurysms (RAAs) may occur with a prevalence as high as 10%.

Material and methods:

 

 

Results:

We present the case of a11-year-old Caucasian boy who was admitted with complaints of hypertension and was using propranolol and enalapril. He had no known pathological conditions in medical history and family background. He had no inflammatory syndrome and normal blood tests. No changes were found concerning the plasma cortisol and thyroid hormones levels. The urine analysis revealed no signs of proteins, cellular elements. ABPM revealed diastolic nondipper hypertension and hypertensive drug dosage were titrated accordingly. The initial performed abdominal and renal doppler ultrasonographic examination did not show any renal or adrenal pathology.The diagnosis was established incidentally due to an imagistic exam performed for other reasons. There were no end organ damage of heart and eye during four year follow up. A digital subtraction angiography confirmed the left saccular renal artery aneurysms (RAA) and stenosis before the bifurcation and distal left renal artery dysplasia. At follow-up, our patient had percutaneous transluminal renal stent implantation as a definitive treatment.

Conclusions:

In patients with uncontrolled hypertension we should suspect renovascular reasons and examination with CT or MRI angiography reveal the pathology.